Idiopathic Pulmonary Hypertension:

A. Is common
B. Occurs mainly in young men
C. May be present with congenital heart disease
D. Is associated with chest pain, dyspnea and syncope
E. Is seen frequently together with idiopathic systemic hypertension

The Correct answer is D. Is associated with chest pain, dyspnea and syncope

Primary (Idiopathic) Pulmonary Hypertension:

• 2′ to persistently increased fetal pulm HTN
• gradual, irreversible progression
• exertional dyspnea, esp. in adolescence
• X-Ray:
  • lungs usually clear
  • big central PAs, pruned vessels

IPAH occurs at a female-to-male ratio ranging from 2-9:1, depending on the treatment center sampled; however, the reasons for this female predilection remain unknown.

• The most common symptoms reported in a national prospective study by Rich, et al in 1987 are as follows:
• Dyspnea is present in 60%.
• Weakness is present in 19%.
• Recurrent syncope is present in 13%.
• Women are more likely to be symptomatic than men.