A 2 year old boy with Tetralogy of Fallot is showing the following sign:

A. Cyanosis
B. Hypertrophic left ventricle
C. Hypertrophic left atrium
D. Hypertrophic media of pulmonary arterioles
E. Hypertrophic media of pulmonary veins

The Correct Answer is A. Cyanosis

FEATURES OF TETRALOGY OF FALLOT:

  • Most common form of cyanotic heart disease; 6-10% of all congenital heart disease.
  • Constellation of- Large Ventricle Septal Defect, Right Ventricle Outlet Track obstruction (pulmonic stenosis), Aorta override, Right Ventricle Hypertrophy.
  • Degree of cyanosis dependent on degree of Right Ventricle Outlet Track obstruction.
  • Significant RVOT obstruction presents early with cyanosis.
  • Mild RVOT obstruction presents later without cyanosis (pink TET) with murmur.
  • CXR- Boot shaped heart due to RVH.
  • Severe TET with Pulmonary Atresia.
  • Severe stenosis requires PGE to maintain pulmonary blood flow.
  • Initial palliation with systemic to pulmonary shunt in infant with small Pulmonary atresia/stenosis (early BT Shunt).
  • Primary repair in infant with well-formed pulmonary arteries (3-5 months)
  • Asymptomatic (pink) repaired later during the first year.

Meet the Author

Dr. Lawrence Kindo

I am a medical blogger who loves to share interesting health stuff. This blog is dedicated to dissemination of medical MCQs. Enjoy!

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